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Neurovascular Disorders

Birnbaum J, Hellmann DB.

Johns Hopkins Bayview Medical Center, Baltimore, MD, USA.

 Arch Neurol 2009;66:704–9.

Editor’s note: Primary angiitis of the central nervous system (PACNS) is a rare disorder that is characterized by focal (such as transient ischemic attack or stroke) and diffuse (such as headache or encephalopathy) symptoms due to vasculitis of the intracerebral blood vessels. The differential diagnosis of PACNS includes CNS vasculitis secondary to infection and CNS vasculitis in association with systemic vasculitis.

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